Dyke-Davidoff-Masson syndrome is characterized by unilateral atrophy of cerebral hemispheres, enlargement of the ipsilateral sulci, ventricles, and cisternal sp. Dyke-Davidoff-Masson syndrome is a rare condition of unknown frequency resulting from brain injury due to a multitude of causes; especially in. Dyke-Davidoff-Masson Syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere. (hemiatrophy) which is secondary to brain insult.
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Ann Acad Med Singapore. Purchase maeson Subscribe to JN Learning for one year. Vision and hearing were normal, and cranial nerves were intact. Coarctation of midaortic arch presenting with monoparesis. Introduction Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophywhich is usually due to an insult to the developing brain in fetal or early childhood ddyke.
Magnetic resonance imaging of the brain showed unilateral atrophy of the left cerebral hemisphere with dilatation davisoff ipsilateral lateral ventricle and ipsilateral sulcal prominence. Dyke—Davidoff—Masson syndrome in children. These clinical and radiological findings are suggestive of DDMS. Important differential diagnosis includes — Sturge—Weber Syndrome, basal cell germinoma, Fishman syndrome, Silver—Russell masdon, linear nevus syndrome, and Rasmussen encephalitis.
The atrophied cerebral hemisphere will have prominent sulcal spaces if the insult occurs after birth or after the end of sulcation. The convulsion was followed by decreased movement of the right side of the body and drooling of saliva from the right side occasionally, for which the patient was given some native medication. These findings were suggestive of the diagnosis of DDMS.
Cerebral hemiatrophy, Dgke syndrome, hemiparesis. The human brain reaches half of its adult size during the first year of dhke and three fourth of the adult size is attained by the end of 3 years. This syndrome is usually seen during adolescence; however, it can also be seen in childhood. Dyke—Davidoff—Masson syndrome DDMS is described jasson skull radiographic and pneumatoencephalographic changes in their series of nine patients whose clinical characteristics included hemiparesis, seizures, facial asymmetry, and mental retardation which was proposed in by Dyke et al.
There was also mild atrophy of the left cerebral peduncle. Register for email alerts with links to free full-text articles Access PDFs of free articles Manage your interests Save searches and receive search alerts.
He had delayed milestones of development in the form of not able to stand or walk and not spoken a word. Copyright American Medical Association. The patient may present with seizure and cerebral imaging may show calcified cortex and hemiatrophy. CT of Cerebral hemiatrophy.
The treatment is symptomatic, and should target convulsion, hemiplegia, hemiparesis, and learning difficulties. Purchase access Subscribe to the journal.
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Create a free personal account to make a comment, download free article PDFs, sign up for alerts and more. The patient did not attend school.
Dyke-Davidoff-Masson syndrome | Radiology Reference Article |
The imaging features include unilateral hemispheric atrophy without any calvarial changes. Loading Stack – 0 images remaining. A cerebral cause of arthrogryposis: J Neurosci Rural Pract. National Center for Biotechnology InformationU. He was seizure free for next 3 months but then unfortunately lost for follow-up. The clinical findings may be of variable degree according to dabidoff extent of the brain injury. Get free access to newly published articles.
Dyke–Davidoff–Masson syndrome: A rare cause of cerebral hemiatrophy in children
You can also scroll through stacks with your mouse wheel or the keyboard arrow keys. We present a case of Dyke Davidoff-Masson-syndrome with typical clinical and imaging features. Schweizer Archiv fur Neurologie und Psychiatrie. Here, we report a case of a year-old female child who presented with a single episode of convulsion, mental retardation, and contralateral hemiparesis.
Case 1 Case 1. Temporo-spatial analysis define epileptogenic and functional zone in a case of DDMS.
Sturge-Weber syndrome Sturge-Weber syndrome. InDyke, Davidoff and Masson first described the syndrome in plain radiographic and pneumoencephalographic changes in a series of nine patients. Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophywhich is usually due to an insult to the developing brain in fetal or early childhood period.
Yerdelen D, Masso F.
It can also be due to decreased carotid artery blood flow due to coarctation of aorta. Basal ganglia germinoma with cerebral hemiatrophy. Birth trauma, hypoxia, intracranial hemorrhage, tumors, infections, and prolonged febrile seizures after birth are important dabidoff and post-natal causes.
Disorders of cortical formation: Prognosis is better if hemiparesis occurs after the age of 2 years and without prolonged or repetitive seizures.
Rasmussen encephalitis does not show calvarial changes, and Sturge—Weber syndrome additionally shows enhancing pial angiomas and cortical calcifications.